FDA-filed SPL labeling · retrieved through openFDA

Berotralstat

Berotralstat is an oral plasma kallikrein inhibitor used to prevent attacks of hereditary angioedema (HAE) in adults and children as young as 2 years old.

Brand name Orladeyo
Rx Forms 2 Route Oral
Dr. Brian Staiger, PharmD, BCPS
Reviewed by Last reviewed Jul 21, 2026
🧬 Where this information comes from Click to expand

The clinical label records used on this page are FDA-filed Structured Product Labeling (SPL) retrieved through openFDA. We identified 1 clinical label set within the page’s selected clinical scope after exact ingredient or ingredient-combination matching and applicable route/form matching. Forms, routes, brands, labelers, strengths, and NDC product-record counts are built separately from matching FDA National Drug Code Directory records. The linked DailyMed document is a representative official source for verification, not the page’s only clinical source. View the linked label on DailyMed →

At a glance
Linked label effectiveAug 20, 2026
AvailabilityRx
Earliest approval/marketing year 2018
FDA-listed product records 22
Boxed warningNone found in compared labels
How we combine label and product data →
No current FDA shortage listed · checked Sep 22, 2026
Berotralstat at a glance The quick version — the full detail is in the Patient Information Guide below.
💊
HelloPharmacist Editorial Team Bottom Line
Berotralstat (Orladeyo) is a once-daily oral medication that prevents hereditary angioedema attacks in adults and children as young as 2 by blocking the enzyme responsible for triggering swelling episodes. It is not a rescue treatment, so you still need a separate medication on hand for any attack that does occur. Stick strictly to the prescribed dose — taking more than directed raises the risk of a heart rhythm problem.

📖 Berotralstat: Patient Information Guide

A plain-language walkthrough of Berotralstat — what it treats, how it works, how it’s taken, side effects, warnings and interactions. Tap any section to expand it.

🎯What it's used for

Berotralstat is used specifically to prevent attacks of hereditary angioedema (HAE). Here is the full picture of its approved uses:

  • Orladeyo (berotralstat) is indicated for the prevention (prophylaxis) of HAE attacks in adults and pediatric patients 2 years of age and older.
  • Orladeyo capsules are approved for adults and children aged 12 and older.
  • Orladeyo oral pellets are approved for children aged 2 to less than 12 years, with dosing based on the child's body weight.
  • Orladeyo is not approved to treat an acute (active) HAE attack — it has not been shown to be safe or effective for that purpose.
⚙️How it works

In people with HAE, a protein called C1-inhibitor is deficient or not working properly. This allows an enzyme called plasma kallikrein to run unchecked. When plasma kallikrein is overactive, it breaks down another protein (called high-molecular-weight kininogen) to produce bradykinin — a potent chemical that makes blood vessel walls leaky, causing the swelling and pain of an HAE attack. Berotralstat works by tightly binding to plasma kallikrein and blocking its activity, which keeps bradykinin production under control and reduces how often attacks occur.

💊How it's taken

Orladeyo is taken by mouth once a day with food. Adults and children 12 and older use the capsule form. Children aged 2 to under 12 use the oral pellet packets, with the dose determined by the child's weight.

  • Orladeyo capsules: once daily with a meal.
  • Orladeyo oral pellets: once daily; a meal should be eaten just before or right after the dose. Pellets can be swallowed with a non-acidic drink or sprinkled on a small amount of soft, non-acidic food — consume within 10 minutes.
  • People with moderate or severe liver impairment may need a dose adjustment (capsule form only for adults and patients 12+); children 2 to under 12 with moderate or severe liver impairment should not use Orladeyo.
  • Never take extra doses to prevent an attack or make up for a missed one — always follow your prescriber's instructions.
🤒Side effects — in detail

The most common side effects of Orladeyo — seen in at least 10% of patients — tend to show up early in treatment and usually improve over time:

  • Abdominal (stomach) pain or discomfort
  • Vomiting
  • Diarrhea
  • Back pain
  • Gastroesophageal reflux disease (GERD — stomach acid coming up into the esophagus)

Gut-related side effects were more common at higher doses but typically became less frequent as treatment continued. More rarely, some patients had elevated liver enzymes on blood tests. If stomach side effects persist, contact your doctor — a dose adjustment may help.

⚠️Warnings & precautions
  • Do not take extra doses or go above the prescribed amount. At doses higher than recommended, berotralstat can prolong the QTc interval — an electrical measurement of the heart's rhythm. A prolonged QTc can, in serious cases, lead to dangerous irregular heartbeats. This risk increases as the drug level in your blood rises.
  • Orladeyo will not stop an attack in progress. Always keep a separate rescue medication available for acute HAE attacks.
  • A small number of patients developed elevated liver enzymes during treatment. Your doctor may monitor your liver function with blood tests.
🔀What it interacts with

Berotralstat can affect — and be affected by — several types of medications. Key interactions to know about:

  • P-gp inducers (e.g., certain seizure medications, rifampin): can significantly lower berotralstat levels in the blood, reducing its effectiveness. Avoid combining with Orladeyo.
  • CYP2D6 substrates (many antidepressants, some heart medications, codeine): Orladeyo can raise blood levels of these drugs, increasing their side effects. Your doctor may need to lower the dose of the other medication.
  • CYP3A4 substrates (many common medications, including some statins, certain anxiety or immunosuppressant drugs): same concern — Orladeyo can increase their levels. Monitor closely or adjust dosing.
  • Desogestrel (a hormonal contraceptive): Orladeyo raises levels of its active form in the body. Discuss risks and benefits with your doctor.
  • P-gp substrates (certain heart, cancer, or seizure drugs): at higher-than-recommended doses, Orladeyo can increase their levels. This is another reason never to exceed the prescribed dose.

This is not a complete list of interactions. Always talk with your doctor or pharmacist before starting, stopping, or changing any medication.

📋Before taking it
  • Tell your doctor about every medication, supplement, and herbal product you take before starting Orladeyo — the interaction list is significant.
  • Liver disease: Moderate or severe liver impairment requires a dose reduction (capsules, adults and teens 12+); children 2 to under 12 with moderate or severe liver impairment should not use Orladeyo.
  • Kidney disease: Orladeyo is not recommended for patients with end-stage renal disease. Children aged 2 to under 12 with severe kidney impairment should avoid Orladeyo.
  • Pregnancy: There is limited human safety data. Animal studies did not show birth defects, but discuss the potential risks with your doctor before using Orladeyo during pregnancy.
  • Breastfeeding: It is unknown whether berotralstat passes into human milk. Small amounts were detected in nursing rat pups. Weigh the benefits of breastfeeding against any potential risk with your doctor.
  • Always have an acute HAE rescue treatment available — Orladeyo does not work for attacks that are already happening.
📡Pharmacodynamics — effects in the body

Orladeyo produces a concentration-dependent reduction in plasma kallikrein activity — the more drug present, the greater the suppression of this enzyme. This effect has been measured in HAE patients taking the medication once daily. At the maximum recommended adult dose, no clinically meaningful change in the QTc interval (a heart rhythm measurement) was observed, but at three times that dose, a meaningful QTc prolongation was seen — confirming that the heart-rhythm risk is directly tied to how much drug is in the bloodstream.

🔬Pharmacokinetics — how your body processes it

After taking Orladeyo with food, berotralstat reaches peak blood levels in about 5 hours on average. It builds up gradually in the body, reaching a stable steady-state level within about 6 to 12 days of daily dosing, with roughly 5-fold accumulation at that point. The drug is very extensively bound to proteins in the blood (about 99%) and has a long half-life — typically around 93 hours, meaning it stays in the body for several days after a dose. Berotralstat is broken down mainly by two liver enzymes (CYP2D6 and CYP3A4), and most of it leaves the body through the stool (about 79%), with only a small amount exiting through urine.

📦How to store it

Store at 20°C to 25°C (68°F to 77°F).

📄 Written from Berotralstat’s FDA-approved label information, summarized in plain language with AI, and reviewed by our pharmacy team before publication. Every point is grounded in that labeling — nothing is invented. How we use AI →

🩺 Pharmacist Counseling Corner

Quick, plain-English answers to the questions patients ask most about Berotralstat — the kind of thing our pharmacy team would talk through with you at the counter.

What exactly is Orladeyo supposed to do for me?
Orladeyo is a preventive medication — it works in the background every day to reduce how often your HAE attacks happen. It blocks an enzyme in your blood called plasma kallikrein, which is responsible for triggering the swelling episodes. The goal is fewer attacks over time, not stopping one once it's started. You'll still need a separate rescue medication for any attack that does occur.
Can I take Orladeyo to stop an HAE attack that's happening right now?
No — Orladeyo is not designed or approved to treat an active attack. Taking extra doses to try to stop a flare won't help, and it's actually unsafe because higher doses can affect your heart's electrical rhythm. Always have your acute (rescue) HAE treatment ready, and use that for attacks in progress.
I've been getting stomach issues since starting Orladeyo. Is that normal, and will it get better?
Stomach side effects — like abdominal pain, nausea, vomiting, and diarrhea — are the most commonly reported issues with Orladeyo, especially early on. The good news is they typically ease up as your body adjusts over the first few weeks. If they're really bothering you and not improving, let your doctor know — a dose reduction might help. Don't stop taking it on your own without checking first.
Does it matter if I take this with or without food?
Yes — Orladeyo should always be taken with food. Food doesn't change how much drug your body absorbs overall, but it does affect timing. Taking it with a meal is also important for the pellet form used in younger children. Stick with the same routine each day, and follow whatever your prescriber recommended.
Are there any medications I should be careful about combining with Orladeyo?
Yes, this is important. Orladeyo can raise the blood levels of many other medications — particularly those processed by certain liver enzymes (called CYP2D6 and CYP3A4). That can increase side effects from those other drugs. On the flip side, some medications — like rifampin or certain seizure drugs — can lower Orladeyo levels and make it less effective. Make sure your doctor and pharmacist have a full list of everything you take, including supplements.
Is it safe to take Orladeyo during pregnancy or while breastfeeding?
There isn't enough human data yet to say for certain how Orladeyo affects a developing baby. Animal studies did not find birth defects, but that doesn't tell the whole story for humans. Small amounts may also pass into breast milk based on animal studies. If you're pregnant, planning to become pregnant, or breastfeeding, have an honest conversation with your doctor about the risks and benefits before continuing or starting Orladeyo.
Is Berotralstat available over the counter?
Berotralstat is dispensed by prescription according to its FDA labeling, so it isn't sold over the counter. Your prescriber and pharmacist will determine if it's appropriate for you.
When was Berotralstat first available?
Berotralstat has been available in the United States since at least 2018, based on FDA approval history (Drugs@FDA) and product marketing records.
Who makes Berotralstat?
Berotralstat is supplied by 7 manufacturers listed in the FDA NDC Directory, including BioCryst Pharmaceuticals, Inc., BioCryst Pharmaceuticals Inc., Catalent Pharma Solutions, LLC.

💬 Answers drafted from Berotralstat’s FDA-approved label information, summarized in plain language with AI, and reviewed by our pharmacy team before publication. Grounded in that labeling — nothing is made up. How we use AI →

🧰 Keep exploring

💊 How Berotralstat comes

Berotralstat is available in 2 forms. Different forms and brands can have different approved uses, doses, schedules, and directions. Follow the instructions for your exact product, and do not switch forms without guidance from your prescriber or pharmacist.

Capsule

By mouth
Brands Orladeyo
How this form is used
What it may be used for
  • Orladeyo capsules are used to prevent HAE attacks in adults and pediatric patients 12 years of age and older.
  • Orladeyo capsules are used at a lower dose for adults and patients 12 and older who have moderate or severe liver impairment.
  • Orladeyo capsules may be taken at a lower dose for adults and patients 12 and older who experience persistent stomach or gut side effects.
Important instructions
  • Orladeyo capsules are taken orally once daily with food.
  • Do not take additional doses or doses higher than prescribed — extra doses increase the risk of a heart rhythm problem.
  • Swallow Orladeyo capsules whole; follow your prescriber's instructions for the right dose based on your health.
Available strengths 2 strengths
10 FDA-listed product records

Other oral form

By mouth
Brands Orladeyo
How this form is used
What it may be used for
  • Orladeyo oral pellets are used to prevent HAE attacks in pediatric patients aged 2 years to less than 12 years.
  • Orladeyo oral pellet dose is based on the child's body weight and is taken once daily.
Important instructions
  • Orladeyo oral pellets should not be chewed or crushed — doing so breaks the taste-masking coating and causes a bitter taste.
  • Pour the entire contents of one packet directly into the mouth and swallow immediately with a non-acidic liquid such as water or milk, OR sprinkle over about one tablespoon of soft, non-acidic food (such as mashed potatoes, pureed bananas, or pudding) and eat immediately.
  • Do not use acidic foods like yogurt or applesauce — they dissolve the coating and make the pellets bitter.
  • If pellets are sprinkled on food, they must be consumed within 10 minutes or discarded; a meal should be eaten just before or after giving the pellets.
Available strengths 4 strengths
8 FDA-listed product records

📊 Berotralstat across the U.S. market

How Berotralstat appears in the FDA’s National Drug Code Directory — including its dosage forms, strengths, brand names, manufacturers, and FDA-listed product records. These are directory records, not sales or prescription volume.

2
Dose forms
7
Manufacturers
1
Brand names
22
FDA-listed product records
2018
First marketed

FDA-listed product records by dose form (tablet variants merged) — FDA National Drug Code Directory. Record counts are not sales or prescription volume.

Also listed with the FDA, not a patient dose form: Powder (4) — bulk drug substance sold to compounders/manufacturers and multi-item kits. These aren’t counted in the dose-form total above.

BioCryst Pharmaceuticals, Inc.55%
BioCryst Pharmaceuticals Inc.18%
Catalent Pharma Solutions, LLC9%
Cambrex Charles City, Inc.5%
Cambrex Karlskoga AB5%
Corden Pharma Bergamo SpA5%
Other makers5%

Share of FDA-listed product records by manufacturer — FDA National Drug Code Directory. Record counts are not sales or prescription volume.

📈 How widely Berotralstat is used

A general measure of how commonly Berotralstat is prescribed, based on Medicaid — one of the largest public drug programs. The figure below is prescriptions filled in Q1–Q4 2025, summed across every form and brand of the drug.

Think of this as a proxy for how widely Berotralstat is used, drawn from freely available public data. Medicaid is just one program — these numbers don’t include Medicare, other government coverage, or commercial and cash-pay prescriptions, so real-world use is higher than what’s shown here.

980
Medicaid prescriptions filled (Q1–Q4 2025)
$43.2M gross Medicaid reimbursement (before mandatory rebates — net cost is lower)

How commonly is Berotralstat prescribed? Of the 1,596 medications we measure, Berotralstat ranks #1,284 by Medicaid prescriptions — more than 20% of them.

Where Berotralstat ranks among the drugs we measure · Q1–Q4 2025 · neighbors ±5

Utilization by Berotralstat product

Pick a product to see its own Medicaid numbers. Each chip is one clinical product — a specific strength & dosage form as defined by RxNorm — with brand-name and generic versions combined.

The 150 mg oral capsule is the most-dispensed Berotralstat product — about 98% of these Medicaid prescriptions.

berotralstat 150 MG Oral Capsule Most dispensed

964 Medicaid prescriptions (Q1–Q4 2025) 98% of Berotralstat prescriptions shown $42.5M gross reimbursement (before rebates) ≈ $44,093 per prescription (gross)

Summed across the 1 of 3 listed NDC products with Medicaid activity — every brand and generic of this exact strength & form. RxNorm 2467565

berotralstat 110 MG Oral Capsule

16 Medicaid prescriptions (Q1–Q4 2025) 2% of Berotralstat prescriptions shown $711,897 gross reimbursement (before rebates) ≈ $44,494 per prescription (gross)

Summed across the 1 of 2 listed NDC products with Medicaid activity — every brand and generic of this exact strength & form. RxNorm 2467573

Shares are of the Medicaid prescriptions shown here. Product grouping follows RxNorm (the National Library of Medicine’s drug terminology), so “one product” means one strength & dosage form regardless of manufacturer. Dollar figures are gross Medicaid reimbursement before mandatory rebates — rebates (often large, especially for brand-name drugs) are confidential, so actual net cost to Medicaid is lower than shown.

Source: Medicaid State Drug Utilization Data (CMS), aggregated by generic ingredient — summed across every NDC (all brands, strengths, salt forms and dosage forms) of Berotralstat, and across all states and both fee-for-service and managed-care claims. A general popularity signal; it excludes Medicare, commercial insurance and cash prescriptions, so it is not total U.S. use. Based on the 2 of 5 listed Berotralstat NDCs with Medicaid activity.

🔍 Compare Berotralstat products

A representative set of FDA-listed product records for Berotralstat — across manufacturers, strengths, and dosage forms, grouped by form with each product’s manufacturer and how the FDA approved it. The same medicine may be made and packaged by different companies, so a single drug can have many directory entries. (It’s also why a refill can look different — a new shape, color, or box — even though it contains the same medication.)

Showing 22 of 22 products — FDA National Drug Code Directory. See every product, package size and price: browse all 22 Berotralstat NDCs →

RxNorm Concept Web — From Ingredient to Every Form and Strength

This page starts with one ingredient concept (IN). The branches below show its dose-form concepts (SCDF), then the available clinical drug and strength concepts (SCD). Combination products remain separate concepts with their own pages.

Ingredient (IN) Berotralstat RxCUI 2467540 2 dose forms · 6 strengths
  1. Dose form (SCDF) Oral Capsule RxCUI 2467564 In current FDA listings
    Clinical drug / strength (SCD) 110 MG RxCUI 2467573 150 MG RxCUI 2467565
  2. Dose form (SCDF) Oral Pellet RxCUI 2728873 In current FDA listings
    Clinical drug / strength (SCD) 72 MG RxCUI 2728884 96 MG RxCUI 2728888 108 MG RxCUI 2728874 132 MG RxCUI 2728880

Look up RxCUI 2467540 in the RxCUI Atlas →

RxNorm is the U.S. National Library of Medicine’s normalized drug vocabulary. Its concept hierarchy can include forms that are not currently marketed; the status on each branch compares that concept with current FDA listings. RxCUIs identify vocabulary concepts, not individual packages or manufacturers.

🏷️ Sold under these brand names

Orladeyo

🏭 Manufacturers & labelers

BioCryst Pharmaceuticals, Inc. 12 BioCryst Pharmaceuticals Inc. 4 Catalent Pharma Solutions, LLC 2 Cambrex Charles City, Inc. 1 Cambrex Karlskoga AB 1 Corden Pharma Bergamo SpA 1 Hetero Labs Limited 1

RxNorm drug class

Berotralstat belongs to the Plasma Kallikrein Inhibitor class.

Pharmacologic class Plasma Kallikrein Inhibitor
Drug family (ATC) Drugs used in hereditary angioedema
How it works Cytochrome P450 2D6 Inhibitors, Cytochrome P450 3A4 Inhibitors, Kallikrein Inhibitors, P-Glycoprotein Inhibitors

Classified by RxNorm RxClass — the U.S. National Library of Medicine's standardized drug-classification service (Established Pharmacologic Class from the FDA, the ATC drug family from the WHO, and mechanism of action). Reference only, not medical advice.

🔬 Where this comes from

Core label, product, RxNorm, safety, and utilization data on this page come from the sources identified below. AI-written, editorial, and licensed sections are labeled separately.

📄
FDA-filed drug labels (SPL) Uses, dosing, warnings & side effects from SPL records retrieved through openFDA; the linked representative set can be verified on DailyMed. ✓ Linked label effective Aug 20, 2026
🏭
Forms, brands & labelersAggregated from ingredient-matched FDA National Drug Code Directory product records for Berotralstat.
📈
Real-world reportsThe FDA Adverse Event Reporting System (FAERS), served through openFDA.
🚨
Recalls & shortagesopenFDA drug-enforcement reports and the FDA drug-shortage database.
🧾 Clinical label set — FDA-filed SPL labels retained for Berotralstat after exact ingredient or ingredient-combination matching and applicable route/form matching
Clinical labels in scope
1
NDC products indexed
22
Distinct labelers/manufacturers represented
7
Linked representative label
BioCryst Pharmaceuticals Inc.
Linked label effective
Aug 20, 2026
Composite sections available
21
Linked SPL Set ID
3527ece1-e7e0-40b1-b0c5-6baeb0deabeb
Linked SPL Document ID
3235d554-689b-47e6-9b28-032b051423e2
Open the linked representative label on DailyMed ↗

How we combine label and product data

HelloPharmacist combines public FDA and NLM records; we don’t author the underlying clinical facts. We identified 1 FDA-filed SPL label set within the page’s selected clinical scope after exact ingredient or ingredient-combination matching and applicable route/form matching. The representative label is the starting point for the displayed reference monograph; the 12 largest stored in-scope SPL records, which may include that representative, are compared section by section, and the longest available version of each section is retained. Forms, routes, brands, labelers, product-listed strengths, and product-record counts are aggregated separately from ingredient-matched FDA NDC Directory records; package records listed above are associated with the linked SPL; and the normalized concept hierarchy comes from NLM RxNorm.

For canonical ingredient pages, bounded product-attributed indication and administration excerpts may be added to the AI evidence, and the generator is instructed to preserve available product, brand, route, and form qualifiers instead of treating one label as universal. Where a section is identified as AI-written, its plain-language text is generated from bounded label evidence. New draft drug pages remain in the admin review queue before first publication. BioCryst Pharmaceuticals Inc. is the representative DailyMed label linked for verification and dates; it is not the sole source used for the page.

This is general education, not medical advice — always consult your doctor or pharmacist about your medications and any medical condition. For the exact wording of the linked representative label, view that label on DailyMed; some displayed composite sections may come from other in-scope SPL labels. Learn how we use AI and our data sources & update cadence.